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What is idiopathic pulmonary fibrosis?

Idiopathic pulmonary fibrosis is a type of interstitial lung disease which causes the tissue of the lungs to become thick and stiff.

Affecting 100,000 people in the United States, idiopathic pulmonary fibrosis is a lung disease that causes thickening and scarring to lung tissue, thereby making breathing difficult. People who struggle with it have shortness of breath, among other symptoms, which prevents their brain from receiving enough oxygen.

As a form of interstitial lung disease, idiopathic pulmonary fibrosis targets the interstitium, which is the tissue and space around the air sacs of the lungs.

Every year, up to 40,000 new cases are diagnosed throughout the United States. However, idiopathic pulmonary fibrosis does not affect the airways or the blood vessels in the lungs.

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Source: https://www.cedars-sinai.edu/Education/Medical-Library/